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Year : 2010  |  Volume : 20  |  Issue : 2  |  Page : 114-115

Bilateral renal lymphangioma - An incidental finding

Department of Radiodiagnosis and Surgery, Pt. B D Sharma, PGIMS, Rohtak, Haryana, India

Date of Web Publication9-Jul-2010

Correspondence Address:
S Agarwal
Department of Radiodiagnosis, Pt. BD Sharma, Post Graduate Institute of Medical Sciences, Rohtak
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Source of Support: None, Conflict of Interest: None

DOI: 10.4103/0971-4065.65309

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How to cite this article:
Magu S, Agarwal S, Dalaal S K. Bilateral renal lymphangioma - An incidental finding. Indian J Nephrol 2010;20:114-5

How to cite this URL:
Magu S, Agarwal S, Dalaal S K. Bilateral renal lymphangioma - An incidental finding. Indian J Nephrol [serial online] 2010 [cited 2021 Dec 6];20:114-5. Available from:

Renal lymphangiectasia is a very rare benign disorder of the renal lymphatics. It is known by many different names including renal lymphangiomatosis, parapelvic lymphangiectasia, hygroma renale and polycystic disease of the renal sinus. [1] The origin is unclear and it is generally regarded as a developmental malformation of the renal lymphatic system. It may be seen at any age. Familial association has been reported in some cases. [2] It can be confused clinically, radiologically, and surgically with autosomal dominant polycystic kidney disease in adults, and autosomal recessive polycystic disease in children. However, on imaging, these cysts are large, thin walled, parapelvic and central retroperitoneal in location. Renal parenchyma is relatively normal as against the other two conditions. [2] Clinically, it is usually asymptomatic and incidentally diagnosed. [1]

The complications include hematuria, ascitis, occasional deterioration in renal function and rennin dependent hypertension. [3] The treatment of asymptomatic cases is not required. When collections are very large and causing pressure symptoms, percutaneous drainage may be carried out. [1]

We report the case of a 28-year-old male patient who presented with mild dull aching pain abdomen for the past seven years. There was no other significant history in the past. An ultrasound was performed six years back with aspiration of approximately 20 ml fluid from the lesion for diagnostic purposes and he was diagnosed with renal lymphangioma. He was put on symptomatic treatment and asked to come for regular follow-up. During the present visit his renal functions were normal. Intravenous urography (IVP) revealed normal function bilaterally. However, the calyces were distorted [Figure 1].

Ultrasonography (USG) revealed multiple cysts in the perirenal and peripelvic location, on both sides, distorting the renal outline [Figure 2].

Computed tomography (CT) and magnetic resonance imaging (MRI) revealed that the cysts were non-enhancing and were of cystic density on CT, [Figure 3] while they were of hypo-intermediate signal intensity on T1-weighted images and hyper intense on T2-weighted images [Figure 4] and [Figure 5]. On no imaging modality was the parenchyma of the kidneys involved, however, it appeared markedly reduced in volume at the present visit. In view of the apparent parenchymal compromise, approximately 600 mL of chylous fluid was drained from both sides. The aspirated fluid was rich in protein and contained rennin. On microscopic examination only a few lymphocytes were seen, while no organism was isolated on culture of the fluid.

We present this case to highlight the benign nature of this condition as against the conditions it can be confused with.

  References Top

1.Ashraf K, Raza SS, Ashraf O, Memon W, Memon A, Zubairi TA. Renal lymphangiectasia. Br J Radiol 2007;80:117-8.  Back to cited text no. 1      
2.Meredith WT, Levine E, Ahlstrom NG, Grantham JJ. Exacerbation of familial renal lymphangiomatosis during pregnancy. AJR Am J Roentgenol 1988;151:965-6.   Back to cited text no. 2  [PUBMED]  [FULLTEXT]  
3.Riehl J, Schmitt H, Schδfer L, Schneider B, Sieberth HG. Retroperitoneal lymphangiectasia associated with bilateral renal vein thrombosis. Nephrol Dial Transplant 1997;12:1701-3.  Back to cited text no. 3      


  [Figure 1], [Figure 2], [Figure 3], [Figure 4], [Figure 5]

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